1Department of Allergy and Clinical Immunology, Setubal Hospital Centre, EPE, Setubal, Portugal
2Serviço de Imunoalergologia, Hospital de Santa Maria, Centro Hospitalar Universitário Lisboa Norte, Lisbon, Portugal
3Instituto de Medicina Molecular João Lobo Antunes, Faculdade de Medicina, Universidade de Lisboa, Lisbon, Portugal
4Centro de Imunodeficiências Primárias, Centro Académico de Medicina de Lisboa, Lisbon, Portugal
5Instituto de Patologia, Faculdade de Medicina, Universidade de Lisboa, Lisbon, Portugal
6Department of Gastroenterology, North Lisbon University Hospital Centre, EPE, Lisbon, Portugal
HistoryPublished 18 arch 2022
Accepted: 17 March 2022
Received: 23 December 2021
Common Variable Immunodeficiency; Nodular Regenerative Hyperplasia; non-cirrhotic portal hypertension; alkaline phosphatase; low dose oral budesonide.