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Anaesthetic considerations in paediatric klippel feil syndrome- A case report

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Case Report

Author Details : Shweta Dhiman*, Kavita Rani Sharma

Volume : 7, Issue : 3, Year : 2020

Article Page : 544-546

https://doi.org/10.18231/j.ijca.2020.097

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Abstract

Klippel feil syndrome is a rare skeletal disorder primarily characterized by abnormal union or fusion of
two or more cervical vertebrae which is often associated with cervical canal stenosis. This results in a short
neck, a low hairline at the back of the head, a limited range of motion in the neck and infrequently an
atlanto- axial instability.
Here we report a case of type 3 paediatric Klippel Feil syndrome who underwent Sprengel deformity repair
in prone position and its anesthetic implications.
A careful assessment of airway and an algorithmic approach towards management is needed in children
with KFS. The various spine deformities associated with KFS demand careful positioning and a
reconfirmation of appropriate ETT position, airway pressures and lung compliance is recommended in
these children.

Keywords: Klippel Feil syndrome, Paediatric, Airway management, Prone positioning, Difficult airway.

How to cite : Dhiman S , Sharma K R , Anaesthetic considerations in paediatric klippel feil syndrome- A case report. Indian J Clin Anaesth 2020;7(3):544-546

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