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CC BY-NC-ND 4.0 · Asian J Neurosurg 2021; 16(04): 876-880
DOI: 10.4103/ajns.AJNS_542_20
Case Report

Neurocutaneous melanosis with hydrocephalus and dandy-walker variant

Mohammad Sarwar
Department of Neurosurgery, Medica Institute of Neurological Diseases, Medica Superspecialty Hospital, Kolkata, West Bengal
,
Laxminarayan Tripathy
Department of Neurosurgery, Medica Institute of Neurological Diseases, Medica Superspecialty Hospital, Kolkata, West Bengal
,
Harsh Jain
Department of Neurosurgery, Medica Institute of Neurological Diseases, Medica Superspecialty Hospital, Kolkata, West Bengal
,
Sunandan Basu
Department of Neurosurgery, Medica Institute of Neurological Diseases, Medica Superspecialty Hospital, Kolkata, West Bengal
,
Ashvini Sengupta
1   Department of Laboratory Services, Medica Superspecialty Hospital, Kolkata, West Bengal
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Neurocutaneous melanosis (NCM) is one of the rare, congenital, noninheritable phakomatoses characterized by the presence of large and/or multiple congenital melanocytic cutaneous nevi associated with intracranial leptomeningeal melanocytosis. NCM usually presents before 2 years of age. So far 302 cases have been reported in literature. We report a case of NCM presenting with obstructive hydrocephalus and Dandy-Walker Variant in a young adult.

Key-words:

Dandy-Walker variant - hydrocephalus - neurocutaneous melanosis - tuberculous meningitis

Financial support and sponsorship

Nil.




Publication History

Received: 12 December 2020

Accepted: 30 May 2021

Article published online:
16 August 2022

© 2021. Asian Congress of Neurological Surgeons. This is an open access article published by Thieme under the terms of the Creative Commons Attribution-NonDerivative-NonCommercial License, permitting copying and reproduction so long as the original work is given appropriate credit. Contents may not be used for commercial purposes, or adapted, remixed, transformed or built upon. (https://creativecommons.org/licenses/by-nc-nd/4.0/)

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