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CC BY-NC-ND 4.0 · Indian J Radiol Imaging 2009; 19(02): 151-154
DOI: 10.4103/0971-3026.50841
Neuroradiology

Extraosseous Ewing′s sarcoma / primitive neuroectodermal tumor of the sacral nerve plexus

MK Narula
Department of Radiodiagnosis, Lady Hardinge Medical College, and Associated Smt. Sucheta Kriplani and Kalawati Saran Children Hospital, New Delhi-110 001, India
,
Nishant Gupta
Department of Radiodiagnosis, Lady Hardinge Medical College, and Associated Smt. Sucheta Kriplani and Kalawati Saran Children Hospital, New Delhi-110 001, India
,
Rama Anand
Department of Radiodiagnosis, Lady Hardinge Medical College, and Associated Smt. Sucheta Kriplani and Kalawati Saran Children Hospital, New Delhi-110 001, India
,
Sudhir Kapoor
Department of Orthopedics, Lady Hardinge Medical College, and Associated Smt. Sucheta Kriplani and Kalawati Saran Children Hospital, New Delhi-110 001, India
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Abstract

We report an unusual case of Ewing′s sarcoma / primitive neuroectodermal tumor (PNET) of the sacral nerve plexus in a 9-year-old boy who presented with a soft tissue swelling and severe piercing pain in the lower back region. MRI of the lumbosacral spine showed a lobulated soft tissue mass with clubbed finger-like projections along the path of the sacral nerves, which had caused widening of the spinal canal and the sacral foramina (S2-S4 level). There was presacral extension and posterior scalloping of the sacral vertebrae. Histopathology of the lesion confirmed Ewing′s sarcoma / PNET of the sacral spinal nerve plexus. The patient responded favorably to chemotherapy and radiotherapy, showing clinical and radiological improvement.

Keywords

Extraosseous Ewing’s sarcoma - primitive neuroectodermal tumor - sacral nerve plexus


Publication History

Article published online:
31 July 2021

© 2009. Indian Radiological Association. This is an open access article published by Thieme under the terms of the Creative Commons Attribution-NonDerivative-NonCommercial-License, permitting copying and reproduction so long as the original work is given appropriate credit. Contents may not be used for commercial purposes, or adapted, remixed, transformed or built upon. (https://creativecommons.org/licenses/by-nc-nd/4.0/).

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