Gangliozytisches Paraganglinonom der Papilla Vateri

 

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Zusammenfassung

Es wird über ein blutendendes gangliozytisches Paraganglionom (GPG) der Papilla Vateri eines 47-jährigen Mannes berichtet, das erfolgreich durch eine partielle Duodenopankreatektomie entfernt wurde. GPG des Duodenums sind sehr seltene Tumoren, derzeit wurden 81 Fälle in der Literatur beschrieben. Histologisch finden sich typischerweise drei Zelltypen: epithelioide-, spindelige- und ganglionzell-ähnliche Zellen. Überwiegend handelt es sich um benigne Tumoren. Tumorrezidive und Metastasierung der GPG sind jedoch beschrieben. Das in diesem Fall beobachtete infiltrative Wachstum unterstreicht das maligne Potenzial der GPG.

Abstract

A case of a bleeding duodenal gangliocytic paraganglioma (GPG) of the Papilla Vateri is reported. The 47 year old patient was treated successfully by partial pancreaticoduodenectomy. Histologically the GPG is characterized by three types of cells: epitheloid cells, ganglion-like cells and spindle cells. So far 81 cases are reported in the literature. Most cases of GPGs are benign, metastasis or recurrence is possible. This case showed an infiltrative growth pattern indicating the true neoplastic nature of this tumor.

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Prof. Dr. med. A. Richter

Städtisches Krankenhaus GmbH · Chirurgische Klinik I

Weinberg 1

31134 Hildesheim

Phone: 0 51 21/89-43 48

Fax: 0 51 21/89-45 81