Dtsch Med Wochenschr 2016; 141(S 01): S33-S41
DOI: 10.1055/s-0042-114526
Pulmonale Hypertonie: Empfehlungen der Kölner Konsensus-Konferenz 2016
© Georg Thieme Verlag KG Stuttgart · New York

Gezielte Therapie der pulmonal arteriellen Hypertonie: Empfehlungen der Kölner Konsensuskonferenz 2016

Targeted therapy of pulmonary arterial hypertension: Recommendations of the Cologne Consensus Conference 2016
M. M. Hoeper
1   Klinik für Pneumologie, Medizinische Hochschule, Hannover
2   Deutsches Zentrum für Lungenforschung (DZL)
,
C. Apitz
3   Sektion Kinderkardiologie, Universitätsklinik für Kinder- und Jugendmedizin, Ulm
,
E. Grünig
2   Deutsches Zentrum für Lungenforschung (DZL)
4   Zentrum für Pulmonale Hypertonie, Thoraxklinik am Universitätsklinikum Heidelberg
,
M. Halank
5   Medizinische Klinik I, Universitätsklinikum Carl Gustav Carus an der TU Dresden, Dresden
,
R. Ewert
6   Universitätsmedizin Greifswald, Klinik und Poliklinik für Innere Medizin, Bereich Pneumologie / Infektiologie, Greifswald
,
H. Kaemmerer
7   Klinik für Kinderkardiologie und angeborene Herzfehler, Deutsches Herzzentrum München, Klinik an der Technischen Universität München
,
H.-J. Kabitz
8   II. Medizinische Klinik, Pneumologie, Kardiologie und Internistische Intensivmedizin, Klinikum Konstanz
,
C. Kähler
9   Klinik für Pneumologie, Beatmungsmedizin und Allergologie, Lungenzentrum Süd-West, Wangen im Allgäu
,
H. Klose
10   Centrum für Pulmonale Hypertonie Hamburg, Sektion Pneumologie, Universitätsklinikum Hamburg-Eppendorf
,
H. Leuchte
11   Neuwittelsbach, Klinik der Barmherzigen Schwestern und akademisches Lehrkrankenhaus der LMU München
,
S. Ulrich
12   Klinik für Pneumologie, UniversitätsSpital Zürich, Schweiz
,
K.M. Olsson
1   Klinik für Pneumologie, Medizinische Hochschule, Hannover
2   Deutsches Zentrum für Lungenforschung (DZL)
,
O. Distler
13   Klinik für Rheumatologie, UniversitätsSpital Zürich, Schweiz
,
S. Rosenkranz
14   Klinik III für Innere Medizin und Cologne Cardiovascular Research Center (CCRC), Herzzentrum der Universität zu Köln
,
H.A. Ghofrani
2   Deutsches Zentrum für Lungenforschung (DZL)
15   Universities of Giessen and Marburg Lung Center (UGMLC), Gießen
16   Abteilung für Pneumologie, Kerckhoff-Klinik Bad Nauheim
17   Department of Medicine, Imperial College, London, UK
› Author Affiliations
Further Information

Publication History

Publication Date:
19 October 2016 (online)

Zusammenfassung

Die 2015 veröffentlichen Europäischen Leitlinien zur Diagnostik und Therapie der pulmonalen Hypertonie sind nunmehr auch in Deutschland gültig. Die Leitlinien befassen sich eingehend mit der Therapie der pulmonal arteriellen Hypertonie (PAH). Für die praktische Umsetzung der Europäischen Leitlinien in Deutschland sind jedoch zahlreiche für Deutschland spezifische Gesichtspunkte und bereits wieder neue Daten bedeutsam, die eine ausführliche Kommentierung der Leitlinien und in einigen Punkten eine Aktualisierung notwendig machen. Im Juni 2016 fand in Köln eine Konsensus-Konferenz statt, die von den Arbeitsgruppen PH der Deutschen Gesellschaften für Kardiologie (DGK), Pneumologie (DGP) und Pädiatrische Kardiologie (DGPK) organisiert wurde. Die Konferenz befasste sich mit der Umsetzung der Europäischen Leitlinien in Deutschland. Dazu wurden verschiedene Arbeitsgruppen eingesetzt, von denen sich eine der gezielten Therapie der pulmonal arteriellen Hypertonie (PAH) widmete. Die Ergebnisse und Empfehlungen dieser Arbeitsgruppe werden in dem vorliegenden Manuskript detailliert beschrieben.

Abstract

The 2015 European Guidelines on Diagnosis and Treatment of Pulmonary Hypertension are also valid for Germany. The guidelines contain detailed recommendations for the targeted treatment of pulmonary arterial hypertension (PAH). However, the practical implementation of the European Guidelines in Germany requires the consideration of several country-specific issues and already existing novel data. This requires a detailed commentary to the guidelines, and in some aspects an update already appears necessary. In June 2016, a Consensus Conference organized by the PH working groups of the German Society of Cardiology (DGK), the German Society of Respiratory Medicine (DGP) and the German Society of Pediatric Cardiology (DGPK) was held in Cologne, Germany. This conference aimed to solve practical and controversial issues surrounding the implementation of the European Guidelines in Germany. To this end, a number of working groups was initiated, one of which was specifically dedicated to the targeted therapy of PAH. This article summarizes the results and recommendations of the working group on targeted treatment of PAH.

 
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