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Successful laparoscopic operation of bilateral pheochromocytoma in a patient with Beckwith-Wiedemann syndrome

Journal of Human Hypertension volume 16, pages 281–284 (2002)Cite this article

Abstract

We report the case of a 20-year-old female patient with Beckwith-Wiedemann syndrome presenting with high blood pressure and bilateral adrenal pheochromocytoma successfully removed with laparoscopy in the same time. To our knowledge, the present case is the first observation of a bilateral pheochromocytoma occurring in the Beckwith-Wiedemann syndrome. It provides further support for a genetic anomaly in this condition. Our case also indicates the interest of laparoscopy for the surgical treatment of adrenal pheochromo- cytoma, even in bilateral tumors.

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Authors and Affiliations

  1. Hôpital Saint André, service de Cardiologie/Hypertension artérielle, Bordeaux, France

    L Bémurat, P Gosse, P Lemétayer & J Clémenty

  2. Hôpital Pellegrin, service d'urologie, Bordeaux, France

    P Ballanger

  3. département de pédiatrie, Hôpital Pellegrin-Enfants, Bordeaux, France

    P Barat

  4. département d'anesthésie réanimation III, Hôpital Pellegrin, Bordeaux, France

    P Tauzin-Fin

  5. Hôpital Pellegrin-Enfants, service de génétique médicale, Bordeaux, France

    D Lacombe

Authors
  1. L Bémurat
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  2. P Gosse
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  3. P Ballanger
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  4. P Tauzin-Fin
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  5. P Barat
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  6. D Lacombe
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  7. P Lemétayer
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  8. J Clémenty
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Correspondence to P Gosse.

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Bémurat, L., Gosse, P., Ballanger, P. et al. Successful laparoscopic operation of bilateral pheochromocytoma in a patient with Beckwith-Wiedemann syndrome. J Hum Hypertens 16, 281–284 (2002). https://doi.org/10.1038/sj.jhh.1001378

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  • DOI: https://doi.org/10.1038/sj.jhh.1001378

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