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Hearing loss associated with large internal auditory meatus: a report of five paediatric cases

Published online by Cambridge University Press:  29 June 2007

Catherine S. Birman  and
William P. R. Gibson
Catherine S. Birman*
Affiliation:
New Children's Hospital, Royal Alexandra Hospital for ChildrenSydney, Australia.
William P. R. Gibson
Affiliation:
Department of Surgery, University of Sydney, Sydney, Australia.
*
Address for correspondence: Dr Catherine Birman, 39 Palmerston Road, Hornsby NSW 2077, Australia. Fax: +612 9482 2036.
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Abstract

This paper describes the abnormality of a large internal auditory meatus (LIAM). Computed tomography (CT) scans show the otic capsule to be affected by a widened, bulbar internal auditory meatus with loss of or reduction of the bony wall dividing the lateral fundus of the meatus from the cochlea. The vestibule is abnormally dilated. We report five cases of children with LIAM and profound hearing loss. Three of these children are girls and two children were boys. Three had congenital progressive hearing loss, one of these had an accompanying large vestibular aqueduct and dysplasia of the cochlea. Two patients had had meningitis resulting in profound loss.

Keywords

Hearing loss, sensorineural, aetiologyChildInfantTemporal boneTomography, X-ray computed
Type
Clinical Records
Information
The Journal of Laryngology & Otology , Volume 113 , Issue 11 , November 1999 , pp. 1015 - 1019
Copyright
Copyright © JLO (1984) Limited 1999

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