Case report
Primary Pleural Epithelioid Hemangioendothelioma

https://doi.org/10.1016/j.athoracsur.2010.05.070Get rights and content

Epithelioid hemangioendothelioma is a rare neoplasm of vascular endothelial origin. It can develop in any tissue, but it occurs primarily in the soft tissue, liver, and rarely in the lung. Pulmonary epithelioid hemangioendothelioma can present in the thorax in various manifestations. In the typical pulmonary forms, epithelioid hemangioendothelioma presents as either a solitary nodule, or more often as multiple, small nodules. Pulmonary epithelioid hemangioendothelioma involving the pleural space occurs in patients with disseminated disease [1, 2]. We present a case of primary pleural epithelioid hemangioendothelioma.

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Comment

Pulmonary epithelioid hemangioma was first described as an intravascular bronchioalveolar tumor by Dail and colleagues [1]. It is a rare vascular endothelial tumor that usually presents with multiple, small pulmonary nodules. It affects a broad age range and is evenly distributed throughout one's adult life with a mean age of 40 years [1, 2, 3]. The majority of patients are women [1, 3]. The PEH presents most commonly as an incidental radiographic finding or on workup for nonspecific pulmonary

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    The patient is scheduled to have chemotherapy. Pleura is a rare anatomical site of EHE, and only around 20 cases have been reported in English literature [1–10]. We summarized the cases of pleural EHE in Table 1, by modification from tables in previous reports by Lee et al. [6] and Marquez-Medina et al. [9].

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