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Malignant triton tumor of the duodenum: report of a case

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Abstract

We report a case of malignant triton tumor of the duodenum, which is extremely rare. A submucosal malignant tumor was detected in the duodenum of a 49-year-old woman. The tumor was completely resected by performing pancreaticoduodenectomy. Pathological examination revealed that the lesion was a malignant peripheral nerve sheath tumor with rhabdomyoblastic differentiation, i.e., a malignant triton tumor. Long-term survival has been achieved with no recurrence at 8.5 years after surgery.

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Authors and Affiliations

  1. Department of Gastroenterological Surgery, Japan Community Health Care Organization Sapporo Hokushin Hospital, Atsubetsu-ku, Chuoh 2-jo, 6-2-1, Sapporo, 004-8618, Japan

    Yoh Asahi, Takahito Nakagawa, Kazuki Wakizaka, Ryoji Yokoyama, Manabu Takahashi & Fumiaki Sasaki

  2. Department of Pathology, Japan Community Health Care Organization Sapporo Hokushin Hospital, Atsubetsu-ku, Chuoh 2-jo, 6-2-1, Sapporo, 004-8618, Japan

    Katsuya Nakanishi

  3. Department of Gastroenterology, Japan Community Health Care Organization Sapporo Hokushin Hospital, Atsubetsu-ku, Chuoh 2-jo, 6-2-1, Sapporo, 004-8618, Japan

    Tomofumi Takagi

  4. Department of Radiology, Japan Community Health Care Organization Sapporo Hokushin Hospital, Atsubetsu-ku, Chuoh 2-jo, 6-2-1, Sapporo, 004-8618, Japan

    Hiroyuki Yoshikawa

Authors
  1. Yoh Asahi
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  2. Takahito Nakagawa
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  4. Tomofumi Takagi
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  5. Hiroyuki Yoshikawa
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  8. Manabu Takahashi
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  9. Fumiaki Sasaki
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Correspondence to Takahito Nakagawa.

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Asahi, Y., Nakagawa, T., Nakanishi, K. et al. Malignant triton tumor of the duodenum: report of a case. Int Canc Conf J 7, 52–58 (2018). https://doi.org/10.1007/s13691-018-0320-7

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  • DOI: https://doi.org/10.1007/s13691-018-0320-7

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