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Metachronous Occurrence of Multifocal Phaeochromocytoma

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Abstract

The authors report an 8-yr-old boy who presented with hypertension, psychosis, and visual disturbances due to a left adrenal phaeochromocytoma which was excised. After 4 years, the child developed multifocal phaeochromocytomas in the left suprarenal area, right adrenal gland, and left para-aortic region. The tumors were excised along with re-implantation of normal adrenal tissue from the right adrenal into the omentum. The course of the disease and the family history were suggestive of von Hippel-Lindau (VHL) disease.

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Contributions

VJ and RC were the assistant (VJ), and operating surgeons (RC), involved in the surgical management of the case. In addition, VJ and RC were responsible for collection of data, review of the literature, planning the management of the case, and preparation of the manuscript. AB and VA were directly involved in the medical management of the case in the pediatric intensive care unit and medical ward respectively. KM was involved in the anesthetic management during surgery and in the immediate postoperative period. AP and SRC provided valuable inputs in the management of the case and the preparation and editing of the manuscript.

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Authors and Affiliations

  1. Department of Pediatric Surgery, Lady Hardinge Medical College and Kalawati Saran Children’s Hospital, New Delhi, 110 001, India

    Vishesh Jain, Rajiv Chadha, Archana Puri & Subhasis Roy Choudhury

  2. Department of Pediatrics, Lady Hardinge Medical College and Kalawati Saran Children’s Hospital, New Delhi, 110 001, India

    Amit Bishnoi & Varun Aggarwal

  3. Department of Anesthesiology, Lady Hardinge Medical College and Kalawati Saran Children’s Hospital, New Delhi, 110 001, India

    Kanta Meena

Authors
  1. Vishesh Jain
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  2. Amit Bishnoi
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  3. Kanta Meena
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  4. Varun Aggarwal
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  5. Rajiv Chadha
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  6. Archana Puri
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  7. Subhasis Roy Choudhury
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Correspondence to Vishesh Jain.

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Jain, V., Bishnoi, A., Meena, K. et al. Metachronous Occurrence of Multifocal Phaeochromocytoma. Indian J Pediatr 78, 620–622 (2011). https://doi.org/10.1007/s12098-010-0292-x

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  • DOI: https://doi.org/10.1007/s12098-010-0292-x

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