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Audiological and Speech and Language Characteristics of a Case with Hunter’s Syndrome

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Indian Journal of Otolaryngology and Head & Neck Surgery Aims and scope Submit manuscript

Abstract

Hearing loss is a common manifestation of Hunter’s syndrome, with reported rates ranging from 67.3 to 94%. The aim is to highlight the audiological profile and pathophysiology of mixed hearing loss in individuals with hunter’s syndrome. A 7.6-year-old male child was brought to the department of audiology with a complaint of not responding to name call and regression in the speech and language skills. Detailed audiological showed severe to profound mixed hearing loss. REELS and 3DLAT results showed RLA to be 9 to 10 months and ELA to be 6 to 7 months. Owing to the progressive nature and high prevalence of hearing loss in hunter’s syndrome, this case report highlights the importance of middle ear evaluation in the pediatric hearing assessment apart from OAE and ABR. Speech- language therapy must be considered with a focus on functional communication.

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The author(s) received no financial support for the research.

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Authors and Affiliations

  1. Dept of Audiology and Speech Language Pathology, BASLP, Kasturba Medical College, Manipal Academy of Higher Education, Mangalore, Manipal, India

    Krithi Rao, Prajith Carthik & Aleena Varghese

  2. Dept of Audiology and Speech Language Pathology, Kasturba Medical College, Manipal Academy of Higher Education, Mangalore, Manipal, India

    Divya Seth & Mayur Bhat

Authors
  1. Krithi Rao
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  2. Prajith Carthik
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  3. Aleena Varghese
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  4. Divya Seth
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  5. Mayur Bhat
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Correspondence to Mayur Bhat.

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All procedures performed in the study were in accordance with the ethical standards of the institutional research and ethics committee.

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Rao, K., Carthik, P., Varghese, A. et al. Audiological and Speech and Language Characteristics of a Case with Hunter’s Syndrome. Indian J Otolaryngol Head Neck Surg 76, 1110–1113 (2024). https://doi.org/10.1007/s12070-023-04144-y

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  • DOI: https://doi.org/10.1007/s12070-023-04144-y

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