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Konsensus Diagnose und Therapie von Weichteilsarkomen

Consensus diagnosis and therapy of soft tissue sarcoma

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Summary

Soft tissue sarcomas are heterogeneous tumours and relatively uncommon. There have been advances over the past years concerning pathology, clinical behaviour, diagnosis strategies and the treatment. To summarize these advances as well as making it public is one of the goals of the following consensus guidelines. But why do we need special guidelines for Austria? There are international guidelines published by the European Society of Medical Oncology (ESMO) and the National Comprehensive Cancer Network (NCCN). The cause is that we need an explanation of the matrix the ESMO and the NCCN gave according to our clinical practice, the local requirements and facilities in Austria. The following recommendations were drawn up following a consensus meeting of sarcoma specialists from the three high volume centres located at the medical universities in Austria. All fields of involved physicians from diagnosis to therapy worked together to know that soft tissue sarcomas are an interdisciplinary challenge and multimodal treatment is essential. For this reason, these guidelines not only explain but also give the state of the art and clear recommendations. One of the most important guidelines is that any patient with a suspected soft tissue sarcoma should be referred to one of the three university centres and managed by a specialist sarcoma multidisciplinary team. We hope that the consensus is helpful for the clinical practice and improves the quality of care for patients with soft tissue sarcomas in Austria.

Zusammenfassung

Die Behandlung von Weichteilsarkomen stellt eine interdisziplinäre Herausforderung dar, die eines spezialisierten Zentrums bedarf. Nur bei entsprechender Kooperation von Chirurgen, Strahlentherapeuten und Onkologen mit den diagnostischen Disziplinen Pathologie und Radiologie, ist die Chance auf das beste erreichbare Behandlungsergebnis für einen individuellen Patienten gewährleistet. Voraussetzung einer effizienten Kommunikation ist die Grundkenntnis der Besonderheiten und Klassifikation von Weichteiltumoren, deren Basis eine Unterteilung in drei Dignitätsgruppen (benigne – intermediär – maligne) darstellt. Der Therapieansatz ist in der Regel multimodal und erfordert entsprechende Infrastrukturen und Erfahrung in der Durchführung von komplexen Therapien.

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Authors and Affiliations

  1. Klinische Abteilung für Onkologie, Universitätsklinik für Innere Medizin, Wien, Austria

    Thomas Brodowicz

  2. Klinisches Institut für Pathologie, Medizinische Universität Wien, Austria

    Gabriele Amann

  3. Universitätsklinik für Orthopädie und orthopädische Chirurgie, Graz, Austria

    Andreas Leithner

  4. Universitätsklinik für Strahlentherapie-Radioonkologie, Medizinische Universität Innsbruck, Austria

    Arpad Sztankay

  5. Abteilung für Neuro- und muskuloskeletale Radiologie, Universitätsklinik für Radiodiagnostik, Wien, Austria

    Franz Kainberger

  6. Universitätsklinik für Innere Medizin I, Innsbruck, Austria

    Wolfgang Eisterer

  7. Institut für Pathologie, Medizinische Universität Graz, Austria

    Bernadette Liegl-Atzwanger

  8. Universitätsklinik für Orthopädie, Innsbruck, Austria

    Franz Rachbauer

  9. Klinische Abteilung für Wiederherstellungs- und Plastische Chirurgie, Universitätsklinik für Chirurgie, Wien, Austria

    Thomas Rath

  10. Abteilung für Allgemeinchirurgie, Medizinische Universität Wien, Wien, Austria

    Michael Bergmann

  11. Klinische Abteilung für Onkologie, Universitätsklinik für Innere Medizin, Graz, Austria

    Ferdinand Ploner

  12. Universitätsklinik für Orthopädie, Wien, Austria

    Philipp T. Funovics & Reinhard Windhager

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  1. Thomas Brodowicz
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  2. Gabriele Amann
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  3. Andreas Leithner
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  8. Franz Rachbauer
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  9. Thomas Rath
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  11. Philipp T. Funovics
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  13. Reinhard Windhager
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Correspondence to Thomas Brodowicz.

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Brodowicz, T., Amann, G., Leithner, A. et al. Konsensus Diagnose und Therapie von Weichteilsarkomen. Wien Klin Wochenschr 124, 85–99 (2012). https://doi.org/10.1007/s00508-011-0079-8

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  • DOI: https://doi.org/10.1007/s00508-011-0079-8

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