Abstract
A 10-year-old girl presented with increasing lower back pain without gait or sphincter disturbances. MRI demonstrated a large, intramedullary tumor at the level of the conus. The imaging findings were unlike those of a classic ependymoma or astrocytoma. Histopathologic examination demonstrated clear-cell ependymoma, which is a distinct entity. We found three cases of clear-cell ependymoma of the spinal cord reported in the literature. Clear-cell ependymoma of the spinal cord can be resected completely and needs to be recognized for its imaging features, benign course and favorable prognosis.
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The authors gratefully acknowledge Suzanne Meadows Murphy, B.B.A., for her assistance in manuscript preparation.
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Bapuraj, J.R., Parmar, H.A., Blaivas, M. et al. Imaging features of clear-cell ependymoma of the spinal cord. Pediatr Radiol 37, 384–387 (2007). https://doi.org/10.1007/s00247-007-0413-5
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DOI: https://doi.org/10.1007/s00247-007-0413-5