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Congenital absence of the portal vein in a child with Turner syndrome

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Abstract

Congenital absence of the portal vein (CAPV) is a rare malformation associated with hepatic encephalopathy and liver function abnormalities. We report a case of a 2-year-old with Turner syndrome, CAPV, and congenital heart malformations.

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Acknowledgement

We thank Laura Burton for editing the manuscript.

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Authors and Affiliations

  1. Department of Radiology, University of Tennessee College of Medicine–Chattanooga Branch, Erlanger Health System, 375 E. Third St., Chattanooga, TN, 37403, USA

    Jacob A. Noe & Edward M. Burton

  2. Department of Pediatrics, University of Tennessee College of Medicine–Chattanooga Branch, Erlanger Health System, Chattanooga, TN, USA

    Heather C. Pittman

Authors
  1. Jacob A. Noe
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  2. Heather C. Pittman
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  3. Edward M. Burton
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Corresponding author

Correspondence to Edward M. Burton.

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Noe, J.A., Pittman, H.C. & Burton, E.M. Congenital absence of the portal vein in a child with Turner syndrome. Pediatr Radiol 36, 566–568 (2006). https://doi.org/10.1007/s00247-006-0169-3

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  • DOI: https://doi.org/10.1007/s00247-006-0169-3

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