Skip to main content
SpringerLink
Log in

Cholangitis complicating congenital hepatic fibrosis

  • Case Report
  • Published:
The American Journal of Digestive Diseases Aims and scope Submit manuscript

Summary

A patient with cholangitis complicating congenital hepatic fibrosis is presented. In contrast to most other reported cases, many of whom have been treated surgically, this patient had a benign course. The likelihood that this complication of congenital hepatic fibrosis will respond to appropriate conservative therapy suggests that more aggressive forms of treatment should be reserved for those patients who fail to respond to medical management.

This is a preview of subscription content, log in via an institution to check access.

Access this article

Log in via an institution

Price excludes VAT (USA)
Tax calculation will be finalised during checkout.

Instant access to the full article PDF.

Institutional subscriptions

Similar content being viewed by others

References

  1. Lieberman E, Salinas-Madrigal L, Gwinn JL, Brennan PL: Infantile polycystic disease of the kidneys and liver. Med 50:277–318, 1971

    Google Scholar 

  2. Murray-Lyon IM, Shilkin KB, Laws JW, Illing RC, Williams R: Non-obstructive dilatation of the intrahepatic biliary tree with cholangitis. Q J Med 41:477–489, 1972

    PubMed  Google Scholar 

  3. Murray-Lyon IM, Ockenden BG, Williams R: Congenital hepatic fibrosis—Is it a single entiry? Gastroenterology 64:653–656, 1973

    PubMed  Google Scholar 

  4. Sommerschild HC, Langmark F, Maurseth K: Congenital hepatic fibrosis: Report of two new cases and review of the literature. Surgery 73:53–58, 1973

    PubMed  Google Scholar 

  5. Albukerk J, Duffy JL: Fibrogenesis in congenital hepatic fibrosis. Arch Pathol 92:126–135, 1971

    PubMed  Google Scholar 

  6. Aserkoff BR, Galdabini JJ: Hepatic and renal disease in a young woman. N Engl J Med 290:676–683, 1974

    PubMed  Google Scholar 

  7. Unite I, Maitem A, Bagnasco FM, Irwin GAL: Congenital hepatic fibrosis associated with renal tubular ectasia. Radiology 109:565–570, 1973

    PubMed  Google Scholar 

  8. Caroli J: Diseases of intrahepatic bile ducts. Isr J Med Sci 4:21–35, 1968

    PubMed  Google Scholar 

  9. Turnberg LA, Jones EA, Sherlock S: Biliary secretion in a patient with cystic dilation of the intrahepatic biliary tree. Gastroenterology 54:1155–1161, 1968

    PubMed  Google Scholar 

  10. Erlinger S, Sakellaridis DA, Maillard J, Benhamou JP: Les formes angiocholitiques de la fibrose hepatic congenitale. Presse Med 77: 1189–1191, 1969

    PubMed  Google Scholar 

  11. Tsuchida Y, Ischida M: Dilatation of the intrahepatic bile ducts in congenital cystic dilatation of the common bile duct. Surgery 69:776, 1971

    PubMed  Google Scholar 

  12. Kerr DNS, Harrison DV, Sherlock S, Walker RM: Congenital hepatic fibrosis. Q J Med 30:91–117, 1961

    PubMed  Google Scholar 

  13. McCarthy LJ, Baggenstoss AH, Logan GB: Congenital hepatic fibrosis. Gastroenterology 49:27–36, 1965

    Google Scholar 

  14. Danzinger RG, Hofmann AF, Schoenfield LJ, Thistle JL: Dissolution of cholesterol gallstones by chenodeoxycholic acid. N Engl J Med 286: 1–8, 1972

    PubMed  Google Scholar 

  15. Heap TR, Goldstein GB, Mistilis SP, Stening GF: Communicating cavernous ectasia of intrahepatic ducts. Am J Dig Dis 18:813–819, 1973

    PubMed  Google Scholar 

Download references

Author information

Authors and Affiliations

  1. Department of Medicine, Division of Gastroenterology, University of Florida College of Medicine and Gainesville Veterans Administration Hospital, 32610, Gainesville, Florida

    Stephen A. Howlett MD, Stanford T. Shulman MD, Elia M. Ayoub MD, Ronald A. Alexander MD, William H. Donnelly MD &  James J. Cerda MD, FACP

  2. Departments of Pediatrics and Pathology, University of Florida College of Medicine and Gainesville Veterans Administration Hospital, 32610, Gainesville, Florida

    Stephen A. Howlett MD, Stanford T. Shulman MD, Elia M. Ayoub MD, Ronald A. Alexander MD, William H. Donnelly MD &  James J. Cerda MD, FACP

Authors
  1. Stephen A. Howlett MD
    View author publications

    You can also search for this author in PubMed Google Scholar

  2. Stanford T. Shulman MD
    View author publications

    You can also search for this author in PubMed Google Scholar

  3. Elia M. Ayoub MD
    View author publications

    You can also search for this author in PubMed Google Scholar

  4. Ronald A. Alexander MD
    View author publications

    You can also search for this author in PubMed Google Scholar

  5. William H. Donnelly MD
    View author publications

    You can also search for this author in PubMed Google Scholar

  6. James J. Cerda MD, FACP
    View author publications

    You can also search for this author in PubMed Google Scholar

Additional information

Grant supported by National Institutes of Health grant AM 05664.

Rights and permissions

Reprints and permissions

About this article

Cite this article

Howlett, S.A., Shulman, S.T., Ayoub, E.M. et al. Cholangitis complicating congenital hepatic fibrosis. Digest Dis Sci 20, 790–795 (1975). https://doi.org/10.1007/BF01070839

Download citation

  • Issue Date:

  • DOI: https://doi.org/10.1007/BF01070839

Keywords

Search

Navigation