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Radioembolization for Hepatocellular Carcinoma Arising in the Setting of a Congenital Extrahepatic Portosystemic Shunt (Abernethy Malformation)

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A Correction to this article was published on 21 June 2018

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Abstract

In a 50-year-old male with an incidentally discovered hepatocellular carcinoma, a congenital extrahepatic portosystemic shunt with the absence of the portal vein (Abernethy syndrome) was diagnosed by imaging. This study aims to discuss the variant anatomy relevant to this splanchnic vascular malformation, review its association with the development of liver neoplasms, and report the safety and efficacy of TARE followed by resection for a HCC arising in this rare condition.

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Change history

  • 21 June 2018

    Table 1, which appears below, was inadvertently left out of the published article.

Abbreviations

CT:

Computed tomography

MRI:

Magnetic resonance imaging

CEUS:

Contrast-enhanced ultrasound

TARE:

Transarterial radioembolization

HCC:

Hepatocellular carcinoma

CEPS:

Congentital extrahepatic portosystemic shunt

Ki-67:

Ki-67 protein

AFP:

Alpha fetoprotein

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Authors and Affiliations

  1. Department of Diagnostic and Interventional Radiology and Neuroradiology, Klinikum Augsburg, Stenglinstraße 2, 86156, Augsburg, Germany

    Thomas Kroencke & Hannes Ruhnke

  2. Department of General, Visceral and Transplant Surgery, Klinikum Augsburg, Augsburg, Germany

    Marcus Murnauer

  3. Department of Medical Oncology, Klinikum Augsburg, Augsburg, Germany

    Frank Alexander Jordan

  4. Department of Nuclear Medicine, Klinikum Augsburg, Augsburg, Germany

    Vera Blodow

  5. Institute of Pathology, Klinikum Augsburg, Augsburg, Germany

    Tina Schaller & Bruno Märkl

Authors
  1. Thomas Kroencke
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  2. Marcus Murnauer
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  3. Frank Alexander Jordan
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  4. Vera Blodow
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  5. Hannes Ruhnke
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  6. Tina Schaller
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  7. Bruno Märkl
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Corresponding author

Correspondence to Thomas Kroencke.

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Conflict of interest

The corresponding author received an honorarium from the speakers’ bureau of Sirtex Medical. All other coauthors of the manuscript report no conflict of interest.

Ethical Approval

For this type of study IRB approval was granted.

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Informed consent for this publication was obtained from the patient.

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Kroencke, T., Murnauer, M., Jordan, F.A. et al. Radioembolization for Hepatocellular Carcinoma Arising in the Setting of a Congenital Extrahepatic Portosystemic Shunt (Abernethy Malformation). Cardiovasc Intervent Radiol 41, 1285–1290 (2018). https://doi.org/10.1007/s00270-018-1965-5

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  • DOI: https://doi.org/10.1007/s00270-018-1965-5

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