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Two cases of hereditary fructose intolerance

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Abstract

Hereditary fructose intolerance is a rare cause of hepatic cirrhosis in the young. The disorder has a reported frequency of 1 in 20000 live births and no case has been reported from India so far. We report two cases of hereditary fructose intolerance, both with bilateral cataracts and one with cirrhosis of the liver.

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Authors and Affiliations

  1. Dept. of Biochemistry, Kasturba Medical College, Center for Basic Sciences, Bejai, 575004, Mangalore

    N Ananth & G. S. Praveenkumar

  2. Nova Diagnostic and Research Centre, Deralakatte, Mangalore

    K Aravind Rao

  3. K.S. Hegde Medical Academy, Deralakatte, Mangalore

    Vasanthi & Srinivas Kakkilaya

Authors
  1. N Ananth
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  2. G. S. Praveenkumar
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  3. K Aravind Rao
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  4. Vasanthi
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  5. Srinivas Kakkilaya
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Correspondence to N Ananth.

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Ananth, N., Praveenkumar, G.S., Rao, K.A. et al. Two cases of hereditary fructose intolerance. Indian J Clin Biochem 18, 87–92 (2003). https://doi.org/10.1007/BF02867372

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  • DOI: https://doi.org/10.1007/BF02867372

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