Abstract
Two inherited cases of osteomesopyknosis are reported. This is an autosomal dominant osteosclerosis described by Maroteaux in 1980 [2]; its radiological abnormalities consist of increased density of the vertebral plates, pelvis, and sometimes of the upper part of the femur. Osteomesopyknosis, usually discovered incidentally on radiographic examination, is a mild form of familial osteosclerosis and must be distinguished from osteopetrosis which carries a worse prognosis.
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References
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Delcambre, B., Flipo, R.M., Leroux, J.L. et al. Osteomesopyknosis. Skeletal Radiol 18, 21–24 (1989). https://doi.org/10.1007/BF00366765
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DOI: https://doi.org/10.1007/BF00366765