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Kawasaki Disease Shock Syndrome and Mild KD

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Kawasaki Disease

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Abstract

Kawasaki disease shock syndrome (KDSS), although rare, represents the most severe form of Kawasaki disease on the spectrum and is often correlated with profound cardiovascular sequelae. In this chapter, we describe the incidence, pathophysiology, clinical presentation, and diagnostic clues of KDSS and compare it with other types of shock that share similar clinical profiles as well as with hemodynamically stable Kawasaki disease (also called “mild KD”). We also highlight the importance of early therapeutic strategy as this results in better clinical outcomes and lower mortality rates.

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Author information

Authors and Affiliations

  1. China Medical University Children’s Hospital, Taichung, Taiwan

    I-Hsin Tai

  2. Taichung Veterans General Hospital, Taichung, Taiwan

    Yun-Ching Fu

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  1. I-Hsin Tai
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  2. Yun-Ching Fu
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Editor information

Editors and Affiliations

  1. Kawasaki Disease Center, Department of Pediatrics and College of Medicine, Kaohsiung Chang Gung Memorial Hospital and Chang Gung University, Kaohsiung, Taiwan

    Ho-Chang Kuo

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Tai, IH., Fu, YC. (2022). Kawasaki Disease Shock Syndrome and Mild KD. In: Kuo, HC. (eds) Kawasaki Disease. Springer, Singapore. https://doi.org/10.1007/978-981-19-2944-1_18

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  • DOI: https://doi.org/10.1007/978-981-19-2944-1_18

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  • Publisher Name: Springer, Singapore

  • Print ISBN: 978-981-19-2943-4

  • Online ISBN: 978-981-19-2944-1

  • eBook Packages: MedicineMedicine (R0)

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