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Vascular Disorders in the Liver

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Diagnosis of Liver Disease

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Abstract

The components of the hepatic vascular system (hepatic arteries, portal and hepatic veins, sinusoids, and lymphatics) can be damaged by various injuries. Although vascular diseases in the liver are rare conditions, parts of these disorders lead to portal hypertension, hepatic failure, cirrhosis, and hepatocellular carcinoma. The progress of imaging modalities can make the diagnosis for hepatic vascular disorders easier. Imaging plays a crucial role in the early detection and assessment of the extent of hepatic vascular disorders. This article concisely reviews the classification, etiology, pathophysiology, and clinical presentation of hepatic vascular disorders and provides a detailed description of imaging and treatment options, particularly interventional management.

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Change history

  • 12 December 2019

    Chapter 11: E-mail address of Masahiko Koda was not included in the original version. This has been corrected now.

Abbreviations

APF:

Arterioportal fistula

AVM:

Arteriovenous malformations

BCS:

Budd-Chiari syndrome

CDUS:

Color Doppler ultrasonography

CV:

Central vein

EHPVO:

Extrahepatic portal venous obstruction

FALD:

Fontan-associated liver disease

FNH:

Focal nodular hyperplasia

HA:

Hepatic artery

HCC:

Hepatocellular carcinoma

HHT:

Hereditary hemorrhagic telangiectasia

HSCT:

Hematopoietic stem cell transplantation

HV:

Hepatic vein

INCPH:

Idiopathic non-cirrhotic portal hypertension

IVC:

Inferior vena cava

MOVC:

Idiopathic membranous obstruction of IVC

PV:

Portal vein

PVT:

Portal vein thrombosis

RA:

Right atrium

SMAV fistula:

Superior mesenteric arteriovenous fistula

SMV:

Superior mesenteric vein

SV:

Splenic vein

TIPS:

Transjugular intrahepatic portosystemic shunt

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Acknowledgment

We are grateful to Professor Michael A. Kern for constructive advice and helpful suggestions in first edition of this chapter.

Author information

Authors and Affiliations

  1. Tottori, Japan

    Masahiko Koda MD, PhD

  2. Tottori, Japan

    Tomomitsu Matono MD, PhD

  3. Tokyo, Japan

    Makiko Taniai MD, PhD

  4. Kyoto, Japan

    Masaki Iwai MD, PhD

Authors
  1. Masahiko Koda MD, PhD
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  2. Tomomitsu Matono MD, PhD
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  3. Makiko Taniai MD, PhD
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  4. Masaki Iwai MD, PhD
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Corresponding author

Correspondence to Masahiko Koda MD, PhD .

Editor information

Editors and Affiliations

  1. Department of Gastroenterology & Hepatology, Tokyo Women’s Medical University, Shinjuku-ku, Tokyo, Japan

    Etsuko Hashimoto

  2. Department of Gastroenterology/Hepatology, Stanford University School of Medicine, Palo Alto, CA, USA

    Paul Y. Kwo

  3. Department of Pathology and Laboratory Medicine, Dartmouth–Hitchcock Medical Center, Lebanon, NH, USA

    Arief A. Suriawinata

  4. Department of Pathology, Caritas Medical Center, Kowloon, Hong Kong, China

    Wilson M.S. Tsui

  5. Division of Gastroenterology, Hepatology & Internal Medicine, Iwai Clinic, Kamigyo-ku, Kyoto, Japan

    Masaki Iwai

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Koda, M., Matono, T., Taniai, M., Iwai, M. (2019). Vascular Disorders in the Liver. In: Hashimoto, E., Kwo, P., Suriawinata, A., Tsui, W., Iwai, M. (eds) Diagnosis of Liver Disease. Springer, Singapore. https://doi.org/10.1007/978-981-13-6806-6_11

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  • DOI: https://doi.org/10.1007/978-981-13-6806-6_11

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