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The Long QT Syndrome

  • Chapter
Sudden Death

Part of the book series: Developments in Cardiovascular Medicine ((DICM,volume 4))

Abstract

The still inadequate but increasing awareness of the existence of the idiopathic long QT syndrome (LQTS) has provided ample evidence that, as suggested by many, this disease is far from being rare. This notion, coupled with the unusual pathophysiological characteristics and with the high degree of lethality in untreated patients, explains why the LQTS has a rather unique position in the more general problem of sudden death. In fact it seems to provide a mechanistic link between neural and cardiac factors in the genesis of sudden death and represents the most provocative example of neurally mediated, noncoronary sudden cardiac death.

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Authors
  1. P. J. Schwartz
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Editor information

Editors and Affiliations

  1. School of Medicine, Division of Cardiology, University of Liège, Liège, Belgium

    H. E. Kulbertus

  2. Department of Cardiology, Annadal Hospital, University of Limburg, Maastricht, Netherlands

    H. J. J. Wellens

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© 1980 Martinus Nijhoff Publishers bv, The Hague

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Schwartz, P.J. (1980). The Long QT Syndrome. In: Kulbertus, H.E., Wellens, H.J.J. (eds) Sudden Death. Developments in Cardiovascular Medicine, vol 4. Springer, Dordrecht. https://doi.org/10.1007/978-94-009-8834-7_25

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  • DOI: https://doi.org/10.1007/978-94-009-8834-7_25

  • Publisher Name: Springer, Dordrecht

  • Print ISBN: 978-94-009-8836-1

  • Online ISBN: 978-94-009-8834-7

  • eBook Packages: Springer Book Archive

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