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Lymphatic Vascular Malformations of the Limbs: Treatment of Extratruncular Malformations

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Hemangiomas and Vascular Malformations

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Abstract

The development of the Hamburg classification, along with a better understanding of congenital vascular malformations (CVMs), has allowed a more concise description of the lymphatic malformation (LM). The management of LM has become clear: “lymphangioma” should no longer be considered a single LM lesion but rather one of two different LM lesions belonging to an extratruncular lesion, even though the management of lymphangioma is different from its “truncular” LM lesion counterpart that clinically presents as primary lymphedema. Although they often present as discrete clinical entities, the lesions can occur together, making clinical management confusing.

Treatment options for extratruncular lymphangioma should be approached cautiously, as for any other extratruncular CVM lesion, when options such as sclerotherapy and/or surgical excision are being considered.

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Authors and Affiliations

  1. Division of Vascular Surgery, Department of Surgery, George Washington University Medical Center, Washington, DC, USA

    Byung-Boong Lee, James Laredo & Richard F. Neville

Authors
  1. Byung-Boong Lee
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  2. James Laredo
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  3. Richard F. Neville
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Correspondence to Byung-Boong Lee .

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Editors and Affiliations

  1. Department of Vascular Surgery, Center for Vascular Malformations "Stefan Belov", Clinical Institute Humanitas "Mater Domini", Castellanza (Varese), Italy

    Raul Mattassi

  2. Vascular Malformations, Facharztklinik Hamburg, Hamburg, Germany

    Dirk A. Loose

  3. Department of Vascular Surgery, "G. Salvini" Hospital, Garbagnate Milanese (Milan), Italy

    Massimo Vaghi

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Lee, BB., Laredo, J., Neville, R.F. (2015). Lymphatic Vascular Malformations of the Limbs: Treatment of Extratruncular Malformations. In: Mattassi, R., Loose, D., Vaghi, M. (eds) Hemangiomas and Vascular Malformations. Springer, Milano. https://doi.org/10.1007/978-88-470-5673-2_49

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  • DOI: https://doi.org/10.1007/978-88-470-5673-2_49

  • Publisher Name: Springer, Milano

  • Print ISBN: 978-88-470-5672-5

  • Online ISBN: 978-88-470-5673-2

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