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Capillary Nevi and Other Vascular Malformations

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Braun-Falco´s Dermatology

Abstract

With regard to the term “capillary malformation,” deplorable confusion prevails at an international level. The present classification follows the principle that a specific capillary malformation should get a specific name. Capillary nevi include nevus flammeus, port-wine stain of the congenital lipomatous (fatty) overgrowth, vascular malformations, epidermal nevi and scoliosis/skeletal/spinal anomalies (CLOVES) type within PIK3CA-Related Overgrowth Spectrum (PROS), nevus roseus, rhodoid nevus, cutis marmorata telangiectatica congenita, reticular capillary nevus (within PROS), segmental angioma serpiginosum, nevus anemicus, nevus syringocapillaris (so-called “eccrine angiomatous hamartoma”), nevus vascularis mixtus, and angioma circumscriptum. Other less well-established capillary nevi comprise the midfacial port-wine patch of the PROS type, Carter–Mirzaa macules, unilateral punctate telangiectasia, and unilateral nevoid telangiectasia of the patchy type. Moreover, we can distinguish between segmental nevus venosus and hereditary small venous nevi. Lymphatic malformations include the reticular lymphatic nevus and lymphatic cockade malformation (so-called “hobnail hemangioma”). Notably, lymphangioma is a benign proliferative tumor and not a lymphatic malformation.

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Authors and Affiliations

  1. Department of Dermatology, Medical Center–University of Freiburg, Freiburg, Germany

    Rudolf Happle

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  1. Rudolf Happle
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Correspondence to Rudolf Happle .

Editor information

Editors and Affiliations

  1. Department of Dermatology, Venerology and Allergology, University of Munich, Munich, Germany

    Gerd Plewig

  2. Department of Dermatology, Venerology and Allergology, University of Munich, Munich, Germany

    Lars French

  3. Department of Dermatology, Venerology and Allergology, University of Munich, Munich, Germany

    Thomas Ruzicka

  4. Department of Dermatology, Venerology and Allergology, University of Frankfurt, Frankfurt, Germany

    Roland Kaufmann

  5. Department of Dermatology and Allergology, University of Marburg, Marburg, Germany

    Michael Hertl

Section Editor information

  1. Department of Dermatology and Allergology, Philipps University Marburg, Marburg, Germany

    Michael Hertl

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Happle, R. (2022). Capillary Nevi and Other Vascular Malformations. In: Plewig, G., French, L., Ruzicka, T., Kaufmann, R., Hertl, M. (eds) Braun-Falco´s Dermatology. Springer, Berlin, Heidelberg. https://doi.org/10.1007/978-3-662-63709-8_66

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  • DOI: https://doi.org/10.1007/978-3-662-63709-8_66

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  • Publisher Name: Springer, Berlin, Heidelberg

  • Print ISBN: 978-3-662-63708-1

  • Online ISBN: 978-3-662-63709-8

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