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Vasculitis and Vasculopathies

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Braun-Falco´s Dermatology

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Abstract

Vasculitis is inflammation that occurs initially and primarily within the vascular wall. Cutaneous vasculitis can be limited to the skin, such as cutaneous polyarteritis nodosa (PAN) or IgA vasculitis, or reflect a systemic disease (such as systemic PAN or Henoch–Schönlein purpura) and is then an important diagnostic symptom. The clinical picture of the various cutaneous vasculitides is markedly influenced by the size of the mainly affected vessels. In the skin the vasculitides of the small vessels and among them the various immune complex vasculitides are the most frequent. The chapter describes all vasculitides with skin symptoms including therapy. Vasculopathies with partial or complete occlusion of the vessel lumen are the result of embolism or thrombotic occlusion or slowed blood flow, or a pathological change in the vessel wall not caused by vasculitis. Clinically, they are almost all associated with livedo or retiform purpura. The chapter lists the different causes as well as the most important clinical and histological signs.

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Authors and Affiliations

  1. University Hospital for Dermatology and Venerology, Martin Luther University Halle-Wittenberg, Halle (Saale), Germany

    Cord Sunderkötter

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  1. Cord Sunderkötter
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Correspondence to Cord Sunderkötter .

Editor information

Editors and Affiliations

  1. Department of Dermatology, Venerology and Allergology, University of Munich, Munich, Germany

    Gerd Plewig

  2. Department of Dermatology, Venerology and Allergology, University of Munich, Munich, Germany

    Lars French

  3. Department of Dermatology, Venerology and Allergology, University of Munich, Munich, Germany

    Thomas Ruzicka

  4. Department of Dermatology, Venerology and Allergology, University of Frankfurt, Frankfurt, Germany

    Roland Kaufmann

  5. Department of Dermatology and Allergology, University of Marburg, Marburg, Germany

    Michael Hertl

Section Editor information

  1. Centre for Skin Diseases, Marburg, Germany

    Michael Hertl

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Sunderkötter, C. (2022). Vasculitis and Vasculopathies. In: Plewig, G., French, L., Ruzicka, T., Kaufmann, R., Hertl, M. (eds) Braun-Falco´s Dermatology. Springer, Berlin, Heidelberg. https://doi.org/10.1007/978-3-662-63709-8_64

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  • DOI: https://doi.org/10.1007/978-3-662-63709-8_64

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