Zusammenfassung
Tumoren der peripheren Nerven oder im Bereich der peripheren Nerven haben bei neuroprotektivem Vorgehen überwiegend eine gute Prognose. Voraussetzung sind die exakte klinisch-neurologische Diagnostik und adäquate Bildgebung sowie die mikrochirurgische Exploration mit Identifizierung der funktionstragenden Nervenfaszikel und deren funktioneller Schonung. Die Protektion der Nervenfunktion hat generell Priorität vor der Radikalität, insbesondere bei plexiformen Nerventumoren. Die operative Behandlung dient der Diagnosesicherung, der Dekompression der Nerven von der tumorbedingten Kompression und ggf. der Identifizierung der maximalen chirurgischen Therapieoptionen. Die seltenen malignen Nerventumoren erfordern ein schrittweises interdisziplinäres Vorgehen auf sicherer histologischer und molekularbiologischer Grundlage, das die optimalen Therapieziele und individuellen Patientenwünsche berücksichtigt.
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Matthies, C., Heinen, C. (2021). Nerventumoren. In: Antoniadis, G., Harhaus, L., Assmus, H. (eds) Chirurgie peripherer Nerven kompakt. Springer, Berlin, Heidelberg. https://doi.org/10.1007/978-3-662-62504-0_18
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