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Polysaccharide (Amylopectin-like) Storage Myopathy Histochemical, Ultrastructural and Biochemical Studies

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Experimental and Clinical Neuropathology

Part of the book series: Acta Neuropathologica Supplementum ((NEUROPATHOLOGIC,volume 7))

Summary

A case of an adult polysaccharide myopathy is reported in a patient with progressive muscular atrophy and weakness of limb girdles. Histochemistry and electron microscopy showed in some muscle fibers, a storage material composed of amylopectin-like filaments. Biochemical results were normal and no enzyme deficiency was found. This case is compared with three other published cases. Pathological conditons with amylopectin or amylopectin-like storage material are reviewed.

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References

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Author information

Authors and Affiliations

  1. Laboratoire de Neuropathologie, Faculté de Médecine, Marseille, France

    J. F. Pellissier & M. Toga

  2. Laboratoire de Chimie Physiologique and International Institute of Cellular and Molecular Pathology, UCL 7539, Bruxelles, Belgique

    T. de Barsy

  3. Service de Neurologie, Hôpital Saint Joseph, Marseille, France

    J. Bille

  4. Clinique de Rhumatologie et des Maladies neuromusculaires, Hôpital de la Timone, Marseille, France

    G. Serratrice

  5. Laboratoire de Neuropathologie, Faculté de Médecine, 27, Bd Jean Moulin, 13385, Marseille Cedex IV, France

    J. F. Pellissier

Authors
  1. J. F. Pellissier
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  2. T. de Barsy
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  3. J. Bille
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  4. G. Serratrice
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  5. M. Toga
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Editor information

Editors and Affiliations

  1. Ludwig Boltzmann-Institute of Clinical Neurobiology, Lainz-Hospital, Wolkersbergenstraße 1, 1130, Wien, Austria

    Kurt Jellinger (Director) (Director)

  2. Institut für Neuropathologie, Universität Bonn, 5300, Bonn-Venusberg, Germany

    Filippo Gullotta

  3. Institute of Brain Research, Polish Academy of Sciences, 3, ul. Dworkowa, Warsaw, Poland

    Miroslav Mossakowski (Director) (Director)

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© 1981 Springer-Verlag

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Pellissier, J.F., de Barsy, T., Bille, J., Serratrice, G., Toga, M. (1981). Polysaccharide (Amylopectin-like) Storage Myopathy Histochemical, Ultrastructural and Biochemical Studies. In: Jellinger, K., Gullotta, F., Mossakowski, M. (eds) Experimental and Clinical Neuropathology. Acta Neuropathologica Supplementum, vol 7. Springer, Berlin, Heidelberg. https://doi.org/10.1007/978-3-642-81553-9_84

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  • DOI: https://doi.org/10.1007/978-3-642-81553-9_84

  • Publisher Name: Springer, Berlin, Heidelberg

  • Print ISBN: 978-3-540-10449-0

  • Online ISBN: 978-3-642-81553-9

  • eBook Packages: Springer Book Archive

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