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Peripheral Nerve Tumors in Children

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Oncology of CNS Tumors

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Abstract

Peripheral nerve tumors (PNTs), which encompass a diverse pathology, are encountered with rare frequency in children. They are most commonly associated with syndromes, particularly with type 1 neurofibromatosis (NF-1). Adults and children share the same breadth of pathology, yet there are key differences in the relative incidences found in each population. Tumors involving peripheral nerves may be categorized into three broad categories: tumors that arise from the nerve sheath, embryonic neural cells (termed “embryonal”), and multipotent “mesenchymal” soft tissue cells. There have been many classification systems attempting to categorize these tumors. The World Health Organization has published one of the more widely used systems (Table 53.1) [3, 9, 14].

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Authors and Affiliations

  1. Clinical Neurosciences, Division of Neurosurgery, University of Calgary, Foothills Medical Center, Room C1243–1403, 29th Street NW, Calgary, AB T2N 2T9, Canada

    Forrest Hsu & Rajiv Midha

Authors
  1. Forrest Hsu
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  2. Rajiv Midha
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Correspondence to Forrest Hsu .

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Editors and Affiliations

  1. Universitätsklinikum München Klinikum Großhadern Neurochirurgische Klinik, Marchioninistr. 15, München, 81377, Germany

    Jörg-Christian Tonn

  2. Universitätsklinikum Hamburg Krankenhaus Eppendorf Klinik und Poliklinik für Neurochirurgie, Martinistr. 52, Neurologie, Hamburg, 20246, Germany

    Manfred Westphal

  3. Division of Neurosurgery, The Hospital for Sick Children, 555 University Avenue Suite 1502, Toronto, ON, M5G 1X8, Canada

    James T. Rutka

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Hsu, F., Midha, R. (2010). Peripheral Nerve Tumors in Children. In: Tonn, JC., Westphal, M., Rutka, J.T. (eds) Oncology of CNS Tumors. Springer, Berlin, Heidelberg. https://doi.org/10.1007/978-3-642-02874-8_53

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  • DOI: https://doi.org/10.1007/978-3-642-02874-8_53

  • Publisher Name: Springer, Berlin, Heidelberg

  • Print ISBN: 978-3-642-02873-1

  • Online ISBN: 978-3-642-02874-8

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