Abstract
Best vitelliform macular dystrophy (VMD or BVMD) is one of the most common macular dystrophies, affecting 1 in 10,000 individuals. The clinical presentation varies, depending on the stage of the disease at which the patient presents, usually one of these five stages:
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Previtelliform
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Vitelliform (Figs. 16.1, 16.2, 16.3 and 16.4)
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Pseudohypopyon
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Vitelliruptive (Fig. 16.5)
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Atrophic
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Tsang, S.H., Sharma, T. (2018). Best Vitelliform Macular Dystrophy. In: Tsang, S., Sharma, T. (eds) Atlas of Inherited Retinal Diseases. Advances in Experimental Medicine and Biology, vol 1085. Springer, Cham. https://doi.org/10.1007/978-3-319-95046-4_16
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DOI: https://doi.org/10.1007/978-3-319-95046-4_16
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