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Mostly Benign/Rarely Metastasizing

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Management of Soft Tissue Sarcoma

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Abstract

Ossifying fibromyxoid tumor (OFMT) is a very uncommon soft tissue lesion that can occur anywhere in the body, but most commonly in the lower extremity. While most tumors are benign, malignant examples may metastasize in more than half of cases [1]. The largest series to date included only typical cases, excluding tumors with other morphologies, and in that series there were no patients who developed metastatic disease. In the few patients that we have observed recurrences, metastases are observed, typically to lung, and local–regional recurrence can be observed in a multifocal “shotgun” pattern around the area of the tumor, as has been observed in patients with epithelioid sarcoma.

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Authors and Affiliations

  1. International Center Department of Surgery, Memorial Sloan Kettering Cancer Center, New York, NY, USA

    Murray F. Brennan MD

  2. Department of Pathology, Memorial Sloan Kettering Cancer Center, New York, NY, USA

    Cristina R. Antonescu MD

  3. Department of Radiation Oncology, Memorial Sloan Kettering Cancer Center, New York, NY, USA

    Kaled M. Alektiar MD

  4. Monter Cancer Center, Hofstra Northwell School of Medicine and Cold Spring Harbor Laboratory, Lake Success, NY, USA

    Robert G. Maki MD, PhD

Authors
  1. Murray F. Brennan MD
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  2. Cristina R. Antonescu MD
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  3. Kaled M. Alektiar MD
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  4. Robert G. Maki MD, PhD
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Brennan, M.F., Antonescu, C.R., Alektiar, K.M., Maki, R.G. (2016). Mostly Benign/Rarely Metastasizing. In: Management of Soft Tissue Sarcoma. Springer, Cham. https://doi.org/10.1007/978-3-319-41906-0_25

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  • DOI: https://doi.org/10.1007/978-3-319-41906-0_25

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  • Publisher Name: Springer, Cham

  • Print ISBN: 978-3-319-41904-6

  • Online ISBN: 978-3-319-41906-0

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