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Spinal Cord Arteriovenous Shunts in the Pediatric Population

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Textbook of Pediatric Neurosurgery

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Abstract

Spinal cord arteriovenous shunts (SCAVS) are considered to be a rare disease, particularly in pediatric populations. Little information is available in the literature about their natural history, pathogenesis, risk of bleeding, diagnosis, and therapeutic management. Most of the available data were extrapolated from populations including both children and adult patients. Clinical manifestations might be very subtle and difficult to recognize in pediatric patients. Purely genetic syndromes might be correlated with the presence of SCAVS, although these might be included in the development of metameric lesions caused by genetic mutations. A novel classification of the SCAVS has been proposed in accordance with the localization of the shunt itself and four different subtypes have been differentiated: paraspinal, epidural, dural, and intradural. The results following endovascular treatment performed by acrylic embolization in a pediatric population of 31 children between 2012 and 2015 have been reported, allowing the conclusion that treatment of SCAVS in pediatric populations might be considered feasible, safe, and effective if it is performed in experienced centers.

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Author information

Authors and Affiliations

  1. Diagnostic and Therapeutic Neuroradiology, Hôpital Foch, Suresnes, France

    Arturo Consoli & Georges Rodesch

Authors
  1. Arturo Consoli
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  2. Georges Rodesch
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Corresponding author

Correspondence to Georges Rodesch .

Editor information

Editors and Affiliations

  1. International Neuroscience Institute, Hannover, Germany

    Concezio Di Rocco

  2. Oakland Medical Center, Oakland, California, USA

    Dachling Pang

  3. University of Toronto Hospital for Sick Children, Toronto, Ontario, Canada

    James T. Rutka

Section Editor information

  1. Davis; and Kaiser Permanente Hospitals of Northern California, University of California, Oakland, USA

    Dachling Pang

  2. Seoul National University, Seoul, Republic of Korea

    Kyu-Chang Wang

  3. Institute of Child Health, University College London, London, UK

    Dominic Thompson

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Consoli, A., Rodesch, G. (2017). Spinal Cord Arteriovenous Shunts in the Pediatric Population. In: Di Rocco, C., Pang, D., Rutka, J. (eds) Textbook of Pediatric Neurosurgery. Springer, Cham. https://doi.org/10.1007/978-3-319-31512-6_120-1

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  • DOI: https://doi.org/10.1007/978-3-319-31512-6_120-1

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  • Publisher Name: Springer, Cham

  • Print ISBN: 978-3-319-31512-6

  • Online ISBN: 978-3-319-31512-6

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