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Glomus Tumor and Glomangiopericytic Tumors of the Liver

ICD-O code 8711/0

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Tumors and Tumor-Like Lesions of the Hepatobiliary Tract

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Abstract

Glomus tumor is a distinct neoplasm derived from pericyte-like cells normally present in neuromyoarterial structures with the morphology of specialized arteriovenous anastomosis in the skin. These cells normally form glomus bodies involved in thermoregulation and control of hemodynamic features. Glomus tumors are usually benign neoplasms that usually occur in the skin in the vasculature of inner organs and exceptionally in the liver. A distinct neoplasm originating from perivascular myoid cells is termed myopericytoma, glomangiopericytoma, and myofibroma. Most of these unusual neoplasms develop in soft tissues and the skin of children and mid-adult individuals. The tumors very rarely occur in the hepatobiliary tract and the periampullary region, sometimes associated with Epstein-Barr virus infection.

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Authors and Affiliations

  1. University of Bern, Bern, Switzerland

    Arthur Zimmermann

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  1. Arthur Zimmermann
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Correspondence to Arthur Zimmermann .

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Zimmermann, A. (2016). Glomus Tumor and Glomangiopericytic Tumors of the Liver. In: Tumors and Tumor-Like Lesions of the Hepatobiliary Tract. Springer, Cham. https://doi.org/10.1007/978-3-319-26587-2_57-1

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  • DOI: https://doi.org/10.1007/978-3-319-26587-2_57-1

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  • Publisher Name: Springer, Cham

  • Online ISBN: 978-3-319-26587-2

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