Abstract
Double uterus with obstructed hemivagina and ipsilateral renal anomaly (OHVIRA) is a well-described syndrome that most commonly involves a triad of associated anomalies. However, given the rarity of this syndrome in the general population, patients with this syndrome are commonly misdiagnosed and incorrectly managed. It is important for providers to be familiar with the features of this syndrome in order to decrease the time to diagnosis and to ensure that patients receive appropriate counseling regarding management options and long-term outcomes. Once a patient is diagnosed with OHVIRA syndrome, a physician with experience treating this syndrome should be involved in the development of a management plan which should ultimately include surgical correction. In this chapter, we will cover the development and classification of this anomaly, the diagnostic considerations, and the management goals and strategies that providers should understand in order to provide optimal care to patients with OHVIRA syndrome.
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Romanski, P.A., Bortoletto, P., Pfeifer, S.M. (2022). Double Uterus with Obstructed Hemivagina and Ipsilateral Renal Anomaly (OHVIRA). In: Lindheim, S.R., Petrozza, J.C. (eds) Reproductive Surgery. Springer, Cham. https://doi.org/10.1007/978-3-031-05240-8_1
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