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Aortic Arch Anomalies: Aortic Arch Interruption

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Pediatric Cardiac CT in Congenital Heart Disease

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Abstract

The interrupted aortic arch is very rare and occurs in about 1% of the infants with critical congenital heart disease. Perfusion distal to the interruption is dependent on the patency of the ductus arteriosus. Unrecognized and untreated cases have a median age of death at 4–10 days of life. Management of the interruption requires timely diagnosis, use of prostaglandin E infusion immediately after birth to ensure end-organ perfusion, and eventual surgical repair of the interruption. Very rarely there have been cases of patients surviving longer with significant collaterals supplying the lower half of the body. High-quality echocardiography can reveal types of interrupted aortic arch and associated cardiac lesions. Cardiac CT angiogram has played a very important role in delineating details of the interrupted aortic arch, absence/presence of collaterals, intersegmental distance to plan appropriate surgical approaches, and follow-up study to evaluate recurrent coarctation postoperatively.

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Authors and Affiliations

  1. Children’s Heart Institute, Division of Pediatric Cardiology, Children’s Memorial Hermann Hospital, McGovern Medical School, University of Texas Health Science Center at Houston, Houston, TX, USA

    Elisa Rhee

  2. Children’s Heart Institute, Division of Pediatric Cardiology, Non-Invasive Cardiac Imaging, Children’s Memorial Hermann Hospital, McGovern Medical School, University of Texas Health Science Center at Houston, Houston, TX, USA

    Dilachew A. Adebo

Authors
  1. Elisa Rhee
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  2. Dilachew A. Adebo
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Correspondence to Dilachew A. Adebo .

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Editors and Affiliations

  1. Division of Pediatric Cardiology, The University of Texas Health Science Center, Houston, TX, USA

    Dilachew A. Adebo

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Rhee, E., Adebo, D.A. (2021). Aortic Arch Anomalies: Aortic Arch Interruption. In: Adebo, D.A. (eds) Pediatric Cardiac CT in Congenital Heart Disease. Springer, Cham. https://doi.org/10.1007/978-3-030-74822-7_25

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  • DOI: https://doi.org/10.1007/978-3-030-74822-7_25

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  • Publisher Name: Springer, Cham

  • Print ISBN: 978-3-030-74821-0

  • Online ISBN: 978-3-030-74822-7

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