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Pediatric Vascular Anomalies: Opportunities in Primary Care

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Benign Hematologic Disorders in Children

Abstract

Vascular anomalies in children have diverse presentations, exhibit variable patterns of growth and regression, and can develop complications including coagulopathy, disfigurement, and functional impairment. An emerging understanding of the biological basis of different vascular lesions provides opportunities for effective treatment. The goal of this chapter is to familiarize the primary care practitioner with selected, more frequently encountered pediatric vascular anomalies, emphasizing their clinical presentation and natural history. Specific attention is paid to the most common vascular tumor, infantile hemangioma, which can be diagnosed and often managed by the primary pediatric clinician. We then explore opportunities for recognition, imaging, and conservative management of other specific vascular anomalies found in children and discuss indications for referral to subspecialists.

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Acknowledgments

A special thanks is owed to the patients and families who agreed to share their clinical images for this chapter. The author also wishes to thank Drs. Lisa Buckmiller and Mario Ruiz for their mentorship and partnership in the multidisciplinary management of our patients with vascular anomalies.

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Authors and Affiliations

  1. Baylor College of Medicine, The Children’s Hospital of San Antonio, San Antonio, TX, USA

    Adam D. Wolfe

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  1. Adam D. Wolfe
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Correspondence to Adam D. Wolfe .

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Editors and Affiliations

  1. Department of Pediatrics, University of Texas Health Science Center, San Antonio, TX, USA

    Deepak M. Kamat

  2. Department of Pediatrics, Division of Hematology-Oncology, The University of Texas Health Science Center, San Antonio, TX, USA

    Melissa Frei-Jones

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Wolfe, A.D. (2021). Pediatric Vascular Anomalies: Opportunities in Primary Care. In: Kamat, D., Frei-Jones, M. (eds) Benign Hematologic Disorders in Children. Springer, Cham. https://doi.org/10.1007/978-3-030-49980-8_31

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  • DOI: https://doi.org/10.1007/978-3-030-49980-8_31

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