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Management of Conductive Hearing Loss Associated with Aural Atresia and Microtia

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Modern Microtia Reconstruction

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Abstract

Hearing loss associated with craniofacial microsomia (CFM) requires a team approach for evaluation, diagnosis, aural rehabilitation, and surgical intervention. Age-appropriate hearing assessment is essential to appropriately diagnose associated hearing loss and provide early intervention services. Therapy is based on the anomalies associated with the craniofacial microsomia and can vary from ear-level hearing aids to bone conduction sound processors (BCSP), using either band or osseointegrated implant-retention systems to atresia repair. For many patients with favorable anatomy, aural atresia repair allows for improved conductive hearing and quality of life. In summary, unilateral hearing loss (UHL) should be treated early and appropriately to aid in optimal speech and language development, as well as age-appropriate school performance.

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Author information

Authors and Affiliations

  1. Department of Otolaryngology – Head and Neck Surgery, University of Washington School of Medicine, Seattle, WA, USA

    Craig Miller

  2. Pediatric Otolaryngology, Seattle Children’s Hospital, Department of Otolaryngology-Head and Neck Surgery, University of Washington School of Medicine, Seattle, WA, USA

    Randall A. Bly

  3. Pediatric Otolaryngology, Childhood Communication Center, Seattle Childrens Hospital, Department of Otolaryngology – Head and Neck Surgery, University of Washington School of Medicine, Seattle, WA, USA

    Kathleen C. Y. Sie

Authors
  1. Craig Miller
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  2. Randall A. Bly
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  3. Kathleen C. Y. Sie
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Corresponding author

Correspondence to Kathleen C. Y. Sie .

Editor information

Editors and Affiliations

  1. Keck School of Medicine, University of Souther California, Los Angeles, CA, USA

    John F. Reinisch

  2. Plastic and Reconstructive Surgery, Cedars-Sinai Medical Center, Los Angeles, CA, USA

    Youssef Tahiri

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Miller, C., Bly, R.A., Sie, K.C.Y. (2019). Management of Conductive Hearing Loss Associated with Aural Atresia and Microtia. In: Reinisch, J., Tahiri, Y. (eds) Modern Microtia Reconstruction. Springer, Cham. https://doi.org/10.1007/978-3-030-16387-7_9

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  • DOI: https://doi.org/10.1007/978-3-030-16387-7_9

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  • Publisher Name: Springer, Cham

  • Print ISBN: 978-3-030-16386-0

  • Online ISBN: 978-3-030-16387-7

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