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Arthrogryposis multiplex congenita

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Children's Orthopaedics and Fractures

Abstract

Arthrogryposis multiplex congenita literally means multiple curved joints, occurring as a congenital anomaly in the newborn. The first description is ascribed to Otto in 1841 [1]. Sheldon in 1932 published the first detailed description in the United Kingdom and called the condition “amyoplasia congenita” emphasizing the lack of muscle development in this condition [2]. It is important to realize that arthrogryposis is a descriptive term and not an exact diagnosis. Hall who has made a special study of the genetics of the disorder pointed out that there are at least 150 possible diagnoses that can result in multiple curved joint deformities in the newborn child [3]. The reader is referred to Hall for a comprehensive discussion of the disorder [4].

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Authors and Affiliations

  1. Orthopaedic Department, Great Ormond Street Hospital for Sick Children, London, UK

    John A. Fixsen

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  1. John A. Fixsen
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Editor information

Editors and Affiliations

  1. Nuffield Orthopaedic Centre, University of Oxford, Windmill Road, Oxford, OX3 7LD, United Kingdom

    Michael Benson

  2. Sick Children, Great Ormond Street Hospital for, Greater Ormond Street, London, WC1N 3JH, United Kingdom

    John Fixsen

  3. Orthopaedic Hospital, Princess Margaret Rose, Frogston Road West 41-43, Edinburgh, EH10 7ED, United Kingdom

    Malcolm Macnicol

  4. Orthopädie, Olgahospital, Bismarckstr. 8, Stuttgart, 70176, Germany

    Klausdieter Parsch

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Fixsen, J.A. (2010). Arthrogryposis multiplex congenita. In: Benson, M., Fixsen, J., Macnicol, M., Parsch, K. (eds) Children's Orthopaedics and Fractures. Springer, London. https://doi.org/10.1007/978-1-84882-611-3_20

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  • DOI: https://doi.org/10.1007/978-1-84882-611-3_20

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  • Publisher Name: Springer, London

  • Print ISBN: 978-1-84882-610-6

  • Online ISBN: 978-1-84882-611-3

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