Abstract
Hypoplasia of the pulmonary valve (PV) ring and dysplastic PV may exist in rare patients. PV dysplasia is described by thickened and nodular valvular leaflets with no or minimal commissural fusion, hypoplasia of the valve ring, and absence of poststenotic dilation of the pulmonary artery (PA). This entity is associated with the Noonan syndrome, which in turn may be allied to hypertrophic cardiomyopathy [1, 2].
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Alizadehasl, A., Kyavar, M. (2014). Dysplastic Pulmonary Valve Stenosis. In: Sadeghpour, A., Kyavar, M., Alizadehasl, A. (eds) Comprehensive Approach to Adult Congenital Heart Disease. Springer, London. https://doi.org/10.1007/978-1-4471-6383-1_43
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DOI: https://doi.org/10.1007/978-1-4471-6383-1_43
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