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Isolated Pulmonary Langerhans Cell Histiocytosis

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Abstract

Isolated pulmonary involvement in Langerhans Cell Histiocytosis (LCH) is rare in childhood. The authors report a 6-y- old boy presenting with recurrent pneumothorax, whose CT thorax showed diffuse pulmonary cystic lucencies bilaterally. Biopsy of the lesions confirmed pulmonary LCH with Cd1a and S 100 positivity.

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Authors and Affiliations

  1. Department of Pediatrics, Unit 3, Christian Medical College, Vellore, Tamil Nadu, 632004, India

    Sneha Varkki, Mintoo Tergestina, Prabhakar. D Moses & Sophy Korula

  2. Department of Pathology, Christian Medical College, Vellore, Tamil Nadu, India

    Vaishali Sharad Bhonsle

  3. Department of Pediatric Surgery, Christian Medical College, Vellore, Tamil Nadu, India

    John Mathai

Authors
  1. Sneha Varkki
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  2. Mintoo Tergestina
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  3. Vaishali Sharad Bhonsle
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  4. Prabhakar. D Moses
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  5. John Mathai
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  6. Sophy Korula
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Corresponding author

Correspondence to Sophy Korula.

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Varkki, S., Tergestina, M., Bhonsle, V.S. et al. Isolated Pulmonary Langerhans Cell Histiocytosis. Indian J Pediatr 80, 700–703 (2013). https://doi.org/10.1007/s12098-012-0866-x

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  • DOI: https://doi.org/10.1007/s12098-012-0866-x

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