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Solitary Fibrous Tumor of the Liver: a Review of the Current Knowledge and Report of a New Case

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Abstract

Introduction

Solitary fibrous tumors of the liver (SFTL) are uncommon tumors; to the present day, less than 50 cases has been reported in the English scientific literature, most of which behaved as benign tumors. The present article reports a new case of SFTL and has the main purpose of updating the current knowledge of SFTL because due to its rarity, its clinical presentation, study, treatment, and prognosis are not well known. The clinical presentation, radiologic study, surgical treatment, immunohistochemical study, and prognosis are updated and comprehensively discussed.

Methods

Using the common search engines, a search of the English literature was conducted for “Solitary Fibrous Tumor of The Liver,” and the relevant articles were retrieved, reviewed, and analyzed.

Results

All published articles reported anecdotal SFTLs, or SFTLs were included in large series analyzing solitary fibrous tumors on different sites.

Conclusion

The SFTL is an uncommon neoplasm. The clinical presentation is habitually indolent and its behavior is uncertain. In some cases, the SFTL acts as an aggressive sarcoma with poor prognosis. Currently, only surgery offers a therapeutic opportunity for these patients. Due to the lack of current knowledge of long-term behavior of supposedly benign SFTLs and to the lack of specific therapies, methodical long-term follow-up is essential to ensure the survival of patients treated for SFTL.

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  1. Department of Surgery, Hospital San Juan de Dios de La Serena, La Serena, IV Región, Chile

    Marcelo A. Beltrán

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Beltrán, M.A. Solitary Fibrous Tumor of the Liver: a Review of the Current Knowledge and Report of a New Case. J Gastrointest Canc 46, 333–342 (2015). https://doi.org/10.1007/s12029-015-9769-1

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