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Dramatic development of severe SLE in a patient with an incomplete disease

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Abstract

This case report describes the previously-unreported clinical course of a patient with a so-called incomplete systemic lupus erythematosus (SLE), i.e. symptoms related to one organ system only, together with the presence of ANA. He had an indolent course initially and developed, 6 months after the first symptoms, a severe disease with rapid appearance of major and unusual manifestations. The possibility of fast progression and a grave course of an incomplete SLE should be kept in mind. This report is meant to heighten awareness of such an atypical presentation so that prompt and aggressive immunosuppressive therapy may be instituted.

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Acknowledgements

This work was supported by Università degli Studi di Milano (FIRST) and IRCCS Ospedale Maggiore di Milano (Ricerca Corrente).

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Authors and Affiliations

  1. Dipartimento di Medicina Interna, Università degli Studi Milano and IRCCS Ospedale Maggiore Policlinico, Pad. Granelli Via F. Sforza 35, 20122, Milan, Italy

    G Fabio, M. Carrabba, C. Hu & C. Besana

  2. Department of Surgery, IRCCS Ospedale Maggiore Policlinico, Milan, Italy

    M. Floriani

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  1. G Fabio
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  2. M. Carrabba
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  3. C. Hu
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  4. M. Floriani
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  5. C. Besana
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Correspondence to G Fabio.

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Fabio, G., Carrabba, M., Hu, C. et al. Dramatic development of severe SLE in a patient with an incomplete disease. Rheumatol Int 25, 543–547 (2005). https://doi.org/10.1007/s00296-004-0550-1

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  • DOI: https://doi.org/10.1007/s00296-004-0550-1

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