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Incidence of Moyamoya Disease in Denmark: A Population-Based Register Study

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Book cover Trends in the Management of Cerebrovascular Diseases

Part of the book series: Acta Neurochirurgica Supplement ((NEUROCHIRURGICA,volume 129))

Abstract

In this first population-based study of moyamoya disease (MMD) in Europe, the authors identified 56 patients with MMD in Denmark during the period 1994–2015 using nationwide registers. The overall incidence was 0.047 per 100,000 person-years, which is about one-tenth that reported in Japan. Otherwise the epidemiological features were comparable: there was a bimodal age distribution with peaks in the age groups 0–9 years and 30–39 years, with twice as many females as males.

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Author information

Authors and Affiliations

  1. Department of Neurosurgery, Aalborg University Hospital, Aalborg, Denmark

    Peter Birkeland M.D.

  2. Department of Orthopaedic Surgery, Odense University Hospital, Odense, Denmark

    Jens Lauritsen M.D., Ph.D.

  3. Institute of Clinical Research, University of Southern Denmark, Odense, Denmark

    Jens Lauritsen M.D., Ph.D.

Authors
  1. Peter Birkeland M.D.
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  2. Jens Lauritsen M.D., Ph.D.
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Corresponding author

Correspondence to Peter Birkeland M.D. .

Editor information

Editors and Affiliations

  1. Department of Neurosurgery, University Hospital Zurich, University of Zurich, Zurich, Switzerland

    Giuseppe Esposito

  2. Department of Neurosurgery, University Hospital Zurich, University of Zurich, Zurich, Switzerland

    Luca Regli

  3. Department of Neurosurgery, Asahi Uni Murakami Memorial Hospital, Gifu, Japan

    Yasuhiko Kaku

  4. Department of Neurosurgery, National Hospital Organization, Kyoto Medical Center, Kyoto, Japan

    Tetsuya Tsukahara

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For this type of study formal consent is not required.

Conflict of Interest

The authors declare that they have no conflict of interest.

Funding

This study was supported by a grant from Ingeniør K.A. Rohde of Hustrus Legat.

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Birkeland, P., Lauritsen, J. (2018). Incidence of Moyamoya Disease in Denmark: A Population-Based Register Study. In: Esposito, G., Regli, L., Kaku, Y., Tsukahara, T. (eds) Trends in the Management of Cerebrovascular Diseases. Acta Neurochirurgica Supplement, vol 129. Springer, Cham. https://doi.org/10.1007/978-3-319-73739-3_13

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  • DOI: https://doi.org/10.1007/978-3-319-73739-3_13

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  • Publisher Name: Springer, Cham

  • Print ISBN: 978-3-319-73738-6

  • Online ISBN: 978-3-319-73739-3

  • eBook Packages: MedicineMedicine (R0)

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