Primary Intestinal Lymphangiectasia Diagnosed by Chylous Ascites

Hye Ran Kang; Young Kwan Cho; Yun Ju Jo; Yoon Young Jung; Eun Kyung Kim

doi:10.4166/kjg.2016.67.2.116

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Kang, Cho, Jo, Jung, and Kim: Primary Intestinal Lymphangiectasia Diagnosed by Chylous Ascites

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Korean J Gastroenterol 2016;67(2):116-118.

Published online: 4 October 2016

DOI: https://doi.org/10.4166/kjg.2016.67.2.116

Primary Intestinal Lymphangiectasia Diagnosed by Chylous Ascites

Hye Ran Kang, Young Kwan Cho, Yun Ju Jo, Yoon Young Jung¹, Eun Kyung Kim²

Department of Internal Medicine, Eulji University School of Medicine, Seoul, Korea

¹Department of Radiology, Eulji University School of Medicine, Seoul, Korea

²Department of Pathology, Eulji University School of Medicine, Seoul, Korea

Correspondence to: Young Kwan Cho, Department of Internal Medicine, Eulji General Hospital, 68 Hangeulbiseok-ro, Nowon-gu, Seoul 01830, Korea. Tel: +82-2-970-8207, Fax: +82-2-970-8621, E-mail: cyk@eulji.ac.kr

This is an Open Access article distributed under the terms of the Creative Commons Attribution Non-Commercial License (http://creativecommons.org/licenses/by-nc/3.0/) which permits unrestricted non-commercial use, distribution, and reproduction in any medium, provided the original work is properly cited.

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Fig. 1.

Contrastenhanced abdomen CT. Nodularity of inner layer with mucosal enhancement of gastric antrum (white arrow), and ascites (black arrow) are seen.

Fig. 2.

Ascites. There are gross milky color fluids obtained by paracentesis.

Fig. 3.

Lymphangiography. There is no abrupt cut off sign or dermal back flow on lymphatic drainage.

Fig. 4.

Enteroscopic findings. (A) Round elevated lesion with whitish paches. (B) After performing biopsies, white lymphatic fluid was seen flowing out from the biopsy site.

Fig. 5.

Microscopic finding. The pathologic finding of proximal jejunal lesion shows dilated lymphatics containing proteinaceous fluid (H&E, ×200).

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