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CC BY-NC-ND 4.0 · Asian J Neurosurg 2016; 11(02): 170
DOI: 10.4103/1793-5482.145091
CASE REPORT

Management of unusual dysplastic gangliocytoma of the cerebellum (Lhermitte-Duclos disease) in a developing country: Case report and review of the literature

Nyoman Golden
Department of Neurosurgery, Sanglah General Hospital, School of Medicine, Udayana University, Denpasar, Bali
,
Mahadewa Tjokorda
Department of Neurosurgery, Sanglah General Hospital, School of Medicine, Udayana University, Denpasar, Bali
,
Maliawan Sri
Department of Neurosurgery, Sanglah General Hospital, School of Medicine, Udayana University, Denpasar, Bali
,
Wayan Niryana
Department of Neurosurgery, Sanglah General Hospital, School of Medicine, Udayana University, Denpasar, Bali
,
Saputra Herman
1   Department of Pathology, Sanglah General Hospital, School of Medicine, Udayana University, Denpasar, Bali
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Dysplastic cerebellar gangliocytoma or Lhermitte-Duclos disease (LDD) especially in children are extremely rare. In this report we add one further case to this rare entity. A three year old boy with a history of cerebellar and brain stem compression signs was presented in unconscious condition. Computerized tomography (CT) scan revealed a well defined lesion mixed with area of calcification in the right cerebellum and severe obstructive hydrocephalus. Ventricular shunting was performed followed by gross total tumor removal three days after shunting. In the follow up period, the patient showed almost total resolution of all neurological deficits. MRI has been an imaging tool to preoperatively diagnose this disease; otherwise it would be uncertain preoperative diagnosis. However, in this report we would like to emphasize that not all uncertain diagnosis of LDD leads to palliative treatment. Well demarcated lesion may account for the safe surgical resection of this disease.

Key-words:

Cerebellar tumor - dysplastic gangliocytoma - Lhermitte-Duclos disease - surgical resection


Publication History

Article published online:
20 September 2022

© 2016. Asian Congress of Neurological Surgeons. This is an open access article published by Thieme under the terms of the Creative Commons Attribution-NonDerivative-NonCommercial License, permitting copying and reproduction so long as the original work is given appropriate credit. Contents may not be used for commercial purposes, or adapted, remixed, transformed or built upon. (https://creativecommons.org/licenses/by-nc-nd/4.0/)

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