A Case of Endoluminal Stent-Graft for Recurrent Pseudoaneurysms of Aortic Arch Vessels in Behcet's Disease

Behcet's disease is primarily characterized by recurrent orogenital apthous ulcer, uveitis and was first described by a Turkish dermatologist in 1937. 1) As vascular manifestations of Behcet's disease, the venous thrombosis is the most frequent 2) and arterial aneurysm is the most severe complication that can lead to fatality. 3) Recently many authors have described the therapeutic difficulties of arterial complications of Behcet's disease because the recurrent psudoaneurysms are frequent at anastomosis sites following surgical repair. 4) We experienced a case of Behcet's disease complicated with two large pseudoaneuysms at the aortic arch vessels. The larger pseudoaneurysm was located at the anastomosis site of the right common carotid artery connected with the right innominate graft vessel, which developed after aneurysmectomy and graft replacement for primary pseudoaneurysm of the right innominate artery. Another pseudoaneurysm was located at the native vessel of the left subclavian artery. The risk of aneurysmal rupture and obstruction of the upper airway was high because these pseudoaneurysms were leaking continuously and were large-sized. However, these pseudoaneurysms were completely resolved at the follow-up CT scan following effective percutaneous endovascular intervention with stent-graft CT.