J Korean Med Sci. 2000 Feb;15(1):103-104. English.
Published online Apr 24, 2009.
https://doi.org/10.3346/jkms.2000.15.1.103
Published online Apr 24, 2009.
https://doi.org/10.3346/jkms.2000.15.1.103
Copyright © 2000 The Korean Academy of Medical Sciences
Case Report
Successful allogeneic bone marrow transplantation for childhood-onset refractory anemia with ringed sideroblasts
Hoon Kook,
Chan Jong Kim,
Won Sang Yoon,
Dong Wook Ryang,*
and Tai Ju Hwang
Abstract
Refractory anemia with ringed sideroblasts (RARS) is an extremely rare type of myelodysplastic syndrome in children. We describe a 10-year-old boy with RARS presented with pancytopenia. He remained relatively stable with only a few transfusions until age of 20 years, when he underwent an allogeneic bone marrow transplantation (BMT) because of increased transfusion requirements. He remains in complete chimeric state at 20 months posttransplant with normal hematologic parameters. To our knowledge, this is the first description of successful BMT in a patient with childhood-onset RARS. The indication of BMT for this rare disorder in children is discussed.
Keywords
Anemia Sideroblastic; Myelodysplastic Syndromes; Child; Bone Marrow Transplantation; Transplantation, Homologous
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MeSH Terms
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