Steakhouse Syndrome in Myotonic Dystrophy

Nobuhiko Ogasawara; Kenichiro Sato; Michiko Tsutsumiuchi; Mami Kanzaki; Yoshikazu Uesaka

doi:10.2169/internalmedicine.9185-17

CASE REPORTS

Steakhouse Syndrome in Myotonic Dystrophy

Nobuhiko Ogasawara, Kenichiro Sato, Michiko Tsutsumiuchi, Mami Kanzaki, Yoshikazu Uesaka

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Keywords: myotonic dystrophy, esophageal occlusion, food bolus impaction, steakhouse syndrome, dysphagia

JOURNAL OPEN ACCESS

2017 Volume 56 Issue 23 Pages 3179-3181

DOI https://doi.org/10.2169/internalmedicine.9185-17

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Abstract

A 70-year-old man with myotonic dystrophy (MD) showed repetitive vomiting and decreased food ingestion. These symptoms were caused by acute mass of steak impaction occluding the esophagus, known as "steakhouse syndrome," which may have occurred in response to esophageal functional changes following gastrointestinal involvement due to MD pathology. The occluding food was successfully removed endoscopically, and his symptoms resolved without relapse. Our case suggests that MD patients can present with "steakhouse syndrome" due to bolus food impaction occluding the esophagus as one of their gastrointestinal manifestations, which underscores the need for its consideration in MD patients presenting with similar symptoms.

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