Autosomal Dominant Polycystic Kidney Disease with Emphysematous Polycystic Renal Infection That Required Surgical Treatment

Kentaro Watanabe; Teruhiro Fujii; Shiho Makabe; Haruno Nakajima; Masayo Sato; Hiroshi Kataoka; Ken Tsuchiya; Kosaku Nitta; Toshio Mochizuki

doi:10.2169/internalmedicine.1257-18

CASE REPORTS

Autosomal Dominant Polycystic Kidney Disease with Emphysematous Polycystic Renal Infection That Required Surgical Treatment

Kentaro Watanabe, Teruhiro Fujii, Shiho Makabe, Haruno Nakajima, Masayo Sato, Hiroshi Kataoka, Ken Tsuchiya, Kosaku Nitta, Toshio Mochizuki

Author information

Kentaro Watanabe
Department of Medicine, Kidney Center, Tokyo Women's Medical University, Japan
Teruhiro Fujii
Department of Medicine, Kidney Center, Tokyo Women's Medical University, Japan
Shiho Makabe
Department of Medicine, Kidney Center, Tokyo Women's Medical University, Japan
Haruno Nakajima
Department of Medicine, Kidney Center, Tokyo Women's Medical University, Japan
Masayo Sato
Department of Medicine, Kidney Center, Tokyo Women's Medical University, Japan
Hiroshi Kataoka
Department of Medicine, Kidney Center, Tokyo Women's Medical University, Japan
Clinical Research Division for Polycystic Kidney Disease, Department of Medicine, Kidney Center, Tokyo Women's Medical University, Japan
Ken Tsuchiya
Department of Blood Purification, Kidney Center, Tokyo Women's Medical University, Japan
Kosaku Nitta
Department of Medicine, Kidney Center, Tokyo Women's Medical University, Japan
Toshio Mochizuki
Department of Medicine, Kidney Center, Tokyo Women's Medical University, Japan
Clinical Research Division for Polycystic Kidney Disease, Department of Medicine, Kidney Center, Tokyo Women's Medical University, Japan

Keywords: autosomal dominant polycystic kidney disease (ADPKD), cystic infection, emphysematous pyelonephritis, emphysematous polycystic renal infection, nephrectomy

JOURNAL OPEN ACCESS

2019 Volume 58 Issue 1 Pages 85-89

DOI https://doi.org/10.2169/internalmedicine.1257-18

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Abstract

We encountered a patient with autosomal dominant polycystic kidney disease (ADPKD) complicated with emphysematous polycystic renal infection (EPRI). A 44-year-old woman visited our hospital for a fever, appetite loss, and gross hematuria. Because the patient was suffering from end-stage renal disease (ESRD), she was immediately hospitalized for hemodialysis. Multiple emphysematous infected cysts were noted in the right kidney, and antibiotic therapy and three rounds of cystic drainage were performed. However, the patient did not respond to treatment. Therefore, laparoscopic right nephrectomy was performed. ADPKD with comorbid EPRI is unresponsive to conservative treatment, and we believe that nephrectomy should be considered.

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