Central nervous system (CNS) involvement in Sjögren syndrome was first described as a condition resembling multiple sclerosis,1 though frequent spinal cord involvement has resulted in the term “Sjögren myelopathy” being used in recent studies.2^–4 Devic disease, or neuromyelitis optica (NMO) was described by Devic in 1894 as a necrotising inflammatory myelopathy associated with optic neuritis (reviewed in Wingerchuck et al, 1999 and 2006).5 6 Revised criteria for Devic disease6 include the presence of optic neuritis, a myelopathy spanning more than three vertebral segments of the cord and the presence of NMO IgG, a recently characterised autoantibody to the …