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An unusual type of combined aortic coarctation due to fibromuscular dysplasia

Published online by Cambridge University Press:  19 August 2008

William A. Suarez ,
Thaddeus W. Kurczynski  and
Edward L. Bove
William A. Suarez*
Affiliation:
Divisions of Pediatric Cardiology and Genetics, Department of Pediatrics, Medical College of Ohio, Toledo, OH, USA, Division of Pediatric Cardiovascular Surgery, University of Michigan, Ann Arbor, MI, USA
Thaddeus W. Kurczynski
Affiliation:
Divisions of Pediatric Cardiology and Genetics, Department of Pediatrics, Medical College of Ohio, Toledo, OH, USA, Division of Pediatric Cardiovascular Surgery, University of Michigan, Ann Arbor, MI, USA
Edward L. Bove
Affiliation:
Divisions of Pediatric Cardiology and Genetics, Department of Pediatrics, Medical College of Ohio, Toledo, OH, USA, Division of Pediatric Cardiovascular Surgery, University of Michigan, Ann Arbor, MI, USA
*
William A. Suarez, MD, Division of Pediatric Cardiology, Medical College of Ohio, 3120 Glendale Avenue, Toledo, OH 43614–5809, USA. Tel: (419) 383 4478; Fax: (419) 383 3567
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Abstract

A 3-year-old patient is described with an unusual form of co-arctation due to hypoplasia of the transverse arch and fibromuscular dysplasia involving a long segment of the thoracic aorta. Surgical repair required resection of the aorta from the distal transverse arch to the mid-descending thoracic aorta, and replacement with a 16-mm Dacron interposition graft. This case demonstrates the importance of preoperative evaluation of the entire aorta in the presence of co-arctation due to fibromuscular dysplasia.

Keywords

Fibromuscular dysplasiaco-arctation of the aortaarterial dysplasia
Type
Brief Reports
Information
Cardiology in the Young , Volume 9 , Issue 3 , May 1999 , pp. 323 - 326
Copyright
Copyright © Cambridge University Press 1999

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